lamellar ichthyosis

lamellar ichthyosis
lamellar ichthyosis n a rare inherited form of ichthyosis characterized by large coarse scales

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ichthyosis lamellaris a genetically and clinically heterogeneous, autosomal recessive form of ichthyosis, in which the affected infant is born encased in a collodionlike membrane (see collodion baby, under baby). The membrane is soon shed, and the skin becomes covered with large, coarse scales, including on all the flexures, the palms, and the soles. Universal erythroderma and pruritus are characteristic, and ectropion of variable degree is usually present.

Lamellar ichthyosis, with thick, brown scales covering the entire skin surface.


Medical dictionary. 2011.

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