ceroid-lipofuscinosis

neuronal ceroid-lipofuscinosis a term for several genetic lipidoses of diverse biochemical and clinical characteristics, all characterized by progressive neurodegeneration, loss of vision, and a fatal course; the infantile type is Haltia-Santavuori disease; the late infantile type is Jansky-Bielschowsky disease; the juvenile type is Vogt-Spielmeyer disease; and the adult type is Kufs disease.