ceramide trihexosidase

ceramide trihexosidase
cer·a·mide tri·hex·o·si·dase (serґə-mīd tri″hek-soґsĭ-dās) α-galactosidase A.

Medical dictionary. 2011.

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  • α-galactosidase A — a lysosomal enzyme that catalyzes the cleavage of terminal galactose residues from glycosphingolipids, particularly ceramide trihexosides. Deficiency of the enzyme, an X linked trait, causes accumulation of ceramide trihexosides and other… …   Medical dictionary

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