β-aminoisobutyricaciduria

β-ami·no·iso·bu·tyr·ic·ac·id·uria (ə-me″no-i″so-bu-tir″ik-as-ĭ-duґre-ə) excessive excretion of R-β-aminoisobutyric acid in the urine, occurring as a benign metabolic variant due to deficiency of β-aminoisobutyrate–pyruvate transaminase; it also occurs in certain illnesses in which rapid tissue destruction and deoxyribonucleic acid catabolism occur. Called also hyper-β-aminoisobutyricaciduria.