α-N-acetylgalactosaminidase

α-N-ac·e·tyl·gal·ac·to·sa·min·i·dase (as″ə-təl-) (as″ə-tēl-gal″ak-tōs″ə-minґĭ-dās) [EC 3.2.1.49] a lysosomal hexosaminidase specifically catalyzing the cleavage of terminal, α-linked, nonreducing N-acetylgalactosamine residues from glycoconjugates. Deficiency of the enzyme, an autosomal recessive trait, is a cause of infantile neuroaxonal dystrophy. Called also α-galactosidase B.