N-acetylgalactosamine-4-sulfatase

N-acetylgalactosamine-4-sulfatase
N-ac·e·tyl·ga·lac·to·sa·mine-4-sul·fa·tase (as″ə-təl-) (as″ə-tēl″gal-ak-tōsґə-mēn sulґfə-tās) [EC 3.1.6.12] a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of sulfate groups from the 4 position of N-acetylgalactosamine residues. The reaction is important in the degradation of dermatan sulfate; deficiency of the enzyme, an autosomal recessive trait, results in Maroteaux-Lamy syndrome (mucopolysaccharidosis VI). Called also arylsulfatase B.

Medical dictionary. 2011.

Игры ⚽ Нужно решить контрольную?

Look at other dictionaries:

  • N-acetylgalactosamine-6-sulfatase — Identifiers EC number 3.1.6.4 CAS number 9025 60 9 …   Wikipedia

  • N-acetylgalactosamine-6-sulfatase — N ac·e·tyl·ga·lac·to·sa·mine 6 sul·fa·tase (as″ə təl ) (as″ə tēl gal″ak tōsґə mēn sulґfə tās) [EC 3.1.6.4] a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of the …   Medical dictionary

  • Sulfatase — Pfam box Symbol = Sulfatase Name = width =200 caption =Steryl sulfatase Pfam= PF00884 InterPro= IPR000917 SMART= PROSITE = PDOC00117 SCOP = 1auk TCDB = OPM family= 24 OPM protein= 1p49 PDB=PDB3|1fsu :43 486 PDB3|1hdhB:3 501 PDB3|1p49A:25… …   Wikipedia

  • Galactosamine-6 sulfatase — Galactosamine (N acetyl) 6 sulfate sulfatase Identifiers Symbols GALNS; FLJ17434; FLJ42844; FLJ98217; GALNAC6S; GAS; MPS4A External IDs …   Wikipedia

  • galactosamine-6-sulfatase — gal·ac·to·sa·mine 6 sul·fa·tase (gal″ak toґsə mēn sulґfə tās) N acetylgalactosamine 6 sulfatase …   Medical dictionary

  • arylsulfatase B — N acetylgalactosamine 4 sulfatase …   Medical dictionary

  • List of EC numbers (EC 3) — This list contains a list of EC numbers for the third group, EC 3, hydrolases, placed in numerical order as determined by the Nomenclature Committee of the International Union of Biochemistry and Molecular Biology.EC 3.1: Acting on Ester BondsEC… …   Wikipedia

  • Hydrolase — Cristal de lysozyme Les hydrolases constituent une classe d enzymes qui catalysent les réactions d hydrolyse de molécules suivant la réaction générale : R R + H2O ⇌ R OH + R H On y trouve par exemple les estérases, qui hydrolysent les …   Wikipédia en Français

  • EC 3.1 — Le groupe EC3.1 est un groupe d hydrolases rassemblant les estérases, c est à dire les enzymes catalysant la réaction générale : R O R + H2O ⇌ R OH + R OH où R représente un acide quelconque et R son substrat. En fonction du milieu, l ester… …   Wikipédia en Français

  • Mucopolysaccharidosis — MPS I redirects here. For zhuyin or bopomofo, a phonetic system for romanizing Chinese, also known as Mandarin Phonetic Symbols I, see Bopomofo. Mucopolysaccharidosis Classification and external resources ICD 10 E76 ICD 9 …   Wikipedia

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”