proteinosis

proteinosis
A state characterized by disordered protein formation and distribution, particularly as manifested by the deposition of abnormal proteins in tissues. [protein + G. -osis, condition]
- lipoid p. [MIM*247100] a disturbance of lipid metabolism in which there are deposits of a protein-lipid complex on the tongue and sublingual and faucial areas leading to hoarseness, and translucent keratotic papillomatous eyelid lesions; autosomal recessive inheritance, frequently with specific intracranial calcifications. SYN: hyalinosis cutis et mucosae, lipoidosis cutis et mucosae, Urbach-Wiethe disease.
- pulmonary alveolar p. a chronic progressive lung disease of adults, characterized by alveolar accumulation of granular proteinaceous material that is PAS-positive and lipid- rich, with little inflammatory cellular exudate; the cause is unknown.

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pro·tein·o·sis .prō-.tē-'nō-səs, -tē-ə- n, pl -o·ses -.sēz or -o·sis·es the accumulation of abnormal amounts of protein in bodily tissues see PULMONARY ALVEOLAR PROTEINOSIS

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pro·tein·o·sis (pro″tēn-oґsis) the accumulation of excess protein in the tissues.

Medical dictionary. 2011.

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  • proteinosis alveolar — Enfermedad que se caracteriza por el depósito de proteínas plasmáticas, lipoproteínas y otros componentes sanguíneos dentro de los alveolos pulmonares. Diccionario Mosby Medicina, Enfermería y Ciencias de la Salud, Ediciones Hancourt, S.A. 1999 …   Diccionario médico

  • proteinosis lipoide — Eng. Lipoid proteinosis Alteración hereditaria que cursa con la presencia de numerosas tumoraciones xantelásmicas en el margen de los párpados (blefarosis moniliforme), aunque también pueden verse afectadas otras áreas de la piel así como la… …   Diccionario de oftalmología

  • proteinosis lipoídica — Eng. Lipidic proteinosis Ver proteinosis lipoide …   Diccionario de oftalmología

  • proteinosis — …   Useful english dictionary

  • Pulmonary alveolar proteinosis — (PAP) is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia),… …   Wikipedia

  • Lipoid proteinosis — Infobox Disease Name = PAGENAME Caption = DiseasesDB = 30808 ICD10 = ICD10|E|78|8|e|70 ICD9 = ICD9|272.8 ICDO = OMIM = 247100 MedlinePlus = eMedicineSubj = derm eMedicineTopic = 241 MeshID = D008065 Lipoid proteinosis is a hyaline skin… …   Wikipedia

  • pulmonary alveolar proteinosis — n a chronic disease of the lungs characterized by the filling of the alveoli with proteinaceous material and by the progressive loss of lung function * * * a chronic lung disease characterized by dyspnea, productive cough, chest pain, weakness,… …   Medical dictionary

  • pulmonary alveolar proteinosis — ▪ pathology       respiratory disorder caused by the filling of large groups of alveoli with excessive amounts of surfactant, a complex mixture of protein and lipid (fat) molecules. The alveoli are air sacs, minute structures in the lungs in… …   Universalium

  • alveolar proteinosis — pulmonary alveolar p …   Medical dictionary

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