methylmalonyl-CoA

methylmalonyl-CoA
An intermediate in the degradation of several metabolites ( e.g., valine, methionine, odd-chain fatty acid s, theronine); elevated in cases of pernicious anemia.
- methylmalonyl-CoA epimerase an enzyme that catalyzes the interconversion of d-methylmalonyl-CoA and l-methylmalonyl-CoA.
- methylmalonyl-CoA mutase an enzyme that catalyzes a reversible interconversion of l-methylmalonyl-CoA and succinyl-CoA; a cobalamin-dependent enzyme; deficiency of this enzyme will result in methylmalonic acidemia.

Medical dictionary. 2011.

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  • Methylmalonyl-CoA — Identifiers CAS number 1264 45 5 …   Wikipedia

  • Methylmalonyl-CoA — Strukturformel Allgemeines Name Methylmalonyl CoA Summenformel …   Deutsch Wikipedia

  • Methylmalonyl-CoA mutase — Rendering based on PDB 2XIJ …   Wikipedia

  • Methylmalonyl-CoA carboxytransferase — Identifiers EC number 2.1.3.1 CAS number 9029 86 1 …   Wikipedia

  • Methylmalonyl CoA epimerase — Ribbon diagram of methylmalonyl CoA epimerase from Propionibacterium shermanii. From PDB 1JC5 …   Wikipedia

  • Methylmalonyl-CoA decarboxylase — Identifiers EC number 4.1.1.41 CAS number 37289 44 4 …   Wikipedia

  • Methylmalonyl-CoA mutase deficiency — Classification and external resources OMIM 251000 DiseasesDB 29509 Methylmalonyl CoA mutase deficiency ( MUT ) is an inborn error of organ …   Wikipedia

  • methylmalonyl-CoA mutase — methylmalonyl CoA mutase. См. метилмалонил КоА мутаза. (Источник: «Англо русский толковый словарь генетических терминов». Арефьев В.А., Лисовенко Л.А., Москва: Изд во ВНИРО, 1995 г.) …   Молекулярная биология и генетика. Толковый словарь.

  • Methylmalonyl-CoA-Mutase — Humane L Methylmalonyl CoA Mutase Bändermodell nach PDB …   Deutsch Wikipedia

  • methylmalonyl-CoA epimerase — meth·yl·mal·o·nyl CoA epim·er·ase (meth″əl malґə nəl ko aґ ə pimґər ās) [EC 5.1.99.1] an enzyme of the isomerase class that catalyzes the equilibration of the D and L isomers of methylmalonyl CoA. The reaction… …   Medical dictionary

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