maleylacetoacetate

maleylacetoacetate
An intermediate in l-phenylalanine and l-tyrosine catabolism; accumulates in certain inherited disorders of tyrosine metabolism.
- m. cis,trans-isomerase an enzyme that catalyzes the reversible conversion of m. to 4-fumarylacetoacetate; an enzyme that participates in l-tyrosine catabolism; a deficiency of this enzyme is associated with tyrosinemia type IB.

Medical dictionary. 2011.

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  • Maleylacetoacetate isomerase — Identifiers EC number 5.2.1.2 CAS number 9023 75 0 …   Wikipedia

  • maleylacetoacetate isomerase — ma·le·yl·ace·to·ac·e·tate isom·er·ase (ma″le əl ə se″to asґə tāt i somґər ās) [EC 5.2.1.2] an enzyme of the isomerase class that catalyzes the interconversion of the isomers 4 maleylacetoacetate and 4… …   Medical dictionary

  • maleylacetoacetate — noun An intermediate in the metabolism of tyrosine …   Wiktionary

  • 4-Maleylacetoacetate — IUPAC name (Z) 4,6 dioxooct 2 enedioic acid …   Wikipedia

  • 4-maleylacetoacetate — 4 ma·le·yl·ace·to·ac·e·tate (ma″le əl ə se″to asґə tāt) an isomer of fumarylacetoacetate, formed by oxidation of homogentisate in the degradation of tyrosine and phenylalanine …   Medical dictionary

  • GSTZ1 — Glutathione transferase zeta 1 (maleylacetoacetate isomerase), also known as GSTZ1, is a human gene.cite web | title = Entrez Gene: GSTZ1 glutathione transferase zeta 1 (maleylacetoacetate isomerase)| url =… …   Wikipedia

  • Homogentisate 1,2-dioxygenase — protein Name=homogentisate 1,2 dioxygenase (homogentisate oxidase) caption= 3D rendering of Homogentisate Dioxygenase with active site amino acid residues and Iron atom colored. Histidine is the tan color, Glutamate the red color, and Iron is the …   Wikipedia

  • Tyrosine — NatOrganicBox name=( S ) 2 Amino 3 (4 hydroxyphenyl) propanoic acid PubChem = 1153 CAS = 60 18 4 SMILES = N [C@@H] (Cc1ccc(O)cc1)C(O)=O C=9 | H=11 | N=1 | O=3 mass=181.19 g/molTyrosine (abbreviated as Tyr or Y) [cite web | author=IUPAC IUBMB… …   Wikipedia

  • Glycine — For the plant, see Glycine (plant). Glycine[1] …   Wikipedia

  • Phenylalanine — Phe redirects here. For other uses, see Phe (disambiguation). Phenylalanine …   Wikipedia

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