iminoglycinuria

A benign inborn error of amino acid transport in renal tubule and intestine; glycine, proline, and hydroxyproline are excreted in the urine; probably autosomal recessive inheritance; genetic heterogeneity is suggested.

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im·i·no·gly·cin·uria -.glī-sə-'nu̇r-ē-ə n an abnormal inherited condition of the kidney associated esp. with hyperprolinemia and characterized by the presence of proline, hydroxyproline, and glycine in the urine

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im·i·no·gly·cin·uria (im″ĭ-no-gli″sin-uґre-ə) a benign, polygenic, autosomal recessive disorder of renal tubular reabsorption of glycine and the imino acids proline and hydroxyproline, marked by excessive levels of all three substances in the urine without clinical symptoms.