fibrodysplasia

fibrodysplasia
- f. ossificans progressiva [MIM*135100] a generalized disorder of connective tissue in which there is ectopic ossification with bone replacing tendons, fasciae, and ligaments; a lethal genetic disorder of autosomal dominant inheritance. SEE ALSO: fibrous dysplasia of bone.

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n.
abnormal development affecting connective tissue.

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fi·bro·dys·pla·sia (fi″bro-dis-plaґzhə) abnormality in development of fibrous connective tissue.

Medical dictionary. 2011.

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  • Fibrodysplasia — may refer to:* Fibrodysplasia ossificans progressiva, a rare disease in which fibrous tissue such as muscle turns to bone when damaged. * Fibromuscular dysplasia, a disease characterized by the fibrous thickening of the renal artery. * Fibrous… …   Wikipedia

  • Fibrodysplasia ossificans progressiva — Infobox Disease Name = Fibrodysplasia ossificans progressiva Caption = DiseasesDB = 8732 ICD10 = ICD10|M|61|1|m|60 ICD9 = ICD9|728.11 ICDO = OMIM = 135100 MedlinePlus = eMedicineSubj = derm eMedicineTopic = 609 MeshID = D009221 Fibrodysplasia… …   Wikipedia

  • Fibrodysplasia ossificans progressiva — Klassifikation nach ICD 10 M61.1 Myositis ossificans progressiva Fibrodysplasia ossificans progressiva …   Deutsch Wikipedia

  • Fibrodysplasia Ossificans Progressiva — Klassifikation nach ICD 10 M61.1 Myositis ossificans progressiva Fibrodysplasia ossificans progressiva …   Deutsch Wikipedia

  • Fibrodysplasia ossificans muliplex progressiva — Klassifikation nach ICD 10 M61.1 Myositis ossificans progressiva Fibrodysplasia ossificans progressiva …   Deutsch Wikipedia

  • fibrodysplasia — noun Abnormal development of fibrous tissue …   Wiktionary

  • fibrodysplasia — n. abnormal development affecting connective tissue …   The new mediacal dictionary

  • fibrodysplasia ossificans progressiva — noun A very rare disease of the connective tissue in which fibrous tissue (including muscle, tendon, and ligament) becomes ossified when damaged …   Wiktionary

  • Fibrodysplasia ossificans progressiva (FOP) — A rare but dramatic genetic disorder that turns muscles, tendons and ligaments into bone, threatening to transform the victim into a statue of stone. FOP is characterized by physical handicap due to bone forming in the wrong places and malformed… …   Medical dictionary

  • fibrodysplasia ossificans progressiva — a rare, progressive, fatal, autosomal dominant disorder caused by mutation of the ACVR1 gene (locus: 2q23 q24), which encodes a receptor that signals a specific transcriptional response related to growth and differentiation. It is characterized… …   Medical dictionary

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