dermatofibrosarcoma protuberans

A relatively slowly growing dermal neoplasm consisting of one or several firm nodules that are usually covered by dark red-blue skin, which tends to be fixed to the palpable masses; histologically, the neoplasm resembles a cellular dermatofibroma with a pronounced storiform pattern; metastases are unusual, but the incidence of recurrence is fairly high.

- pigmented d. an uncommon variant of d. containing heavily pigmented dendritic melanocytes scattered between spindle cells of the tumor. SYN: Bednar tumor, storiform neurofibroma.

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dermatofibrosarcoma pro·tu·ber·ans -prō-'t(y)ü-bə-rənz n a dermal fibroblastic tumor composed of firm nodular masses that usu. do not metastasize

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a tumour probably derived from histiocyte that may occur in any part of the body. It is locally invasive but tends not to metastasize. It often recurs locally despite excision.

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a bulky, protruding, nodular, fibrotic neoplasm in the dermis, usually on the trunk, often extending into the subcutaneous fat; it is locally aggressive and frequently recurs. It is sometimes classified as a type of malignant fibrous histiocytoma.