cystathionine β-synthase

cystathionine β-synthase
An enzyme catalyzing the reversible hydrolysis of l-cystathionine to l-serine and l-homocysteine. A step in cysteine biosynthesis and in methionine catabolism. A deficiency of this enzyme leads to vascular thrombosis, dislocation of ocular lens, and abnormal development. SEE ALSO: cystathionine γ-synthase. SYN: β-thionase, cysteine synthase, serine sulfhydrase.

Medical dictionary. 2011.

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