hereditary pyropoikilocytosis

hereditary pyropoikilocytosis
an autosomal recessive blood disorder in which there are many different types of heat-sensitive poikilocytes and erythrocyte fragments, with severe hemolytic anemia. It resembles severe hereditary elliptocytosis, but there are few if any elliptocytes.

Medical dictionary. 2011.

Игры ⚽ Нужна курсовая?

Look at other dictionaries:

  • Hereditary pyropoikilocytosis — (HPP) is an autosomal recessive form of hemolytic anemia characterized by an abnormal sensitivity of red blood cells to heat and erythrocyte morphology similar to that seen in thermal burns. Patients with HPP tend to experience severe haemolysis… …   Wikipedia

  • Hereditary elliptocytosis — Classification and external resources Blood smear showing elliptocytes ICD 10 D …   Wikipedia

  • Hereditary spherocytosis — This article is about aspects of spherocytosis specific to the hereditary form of the disorder. For details that apply generally to this variant as well as others, see Spherocytosis. Hereditary spherocytosis Classification and external resources… …   Wikipedia

  • pyropoikilocytosis — A rare recessive disorder manifested by severe hemolysis, marked poikilocytosis, and a characteristic sensitivity of the red cells to heat induced fragmentation in vitro; apparently due to a defect in spectrin self association. SYN: hereditary p …   Medical dictionary

  • HPP — hereditary pyropoikilocytosis; history of presenting problems …   Medical dictionary

  • HPP — • hereditary pyropoikilocytosis; • history of presenting problems • human pancreatic polypeptide; • hydroxyphenylpyruvate; • hydroxypyrozo lopyrimidine …   Dictionary of medical acronyms & abbreviations

  • SPTA1 — Spectrin, alpha, erythrocytic 1 (elliptocytosis 2), also known as SPTA1, is a human gene.cite web | title = Entrez Gene: SPTA1 spectrin, alpha, erythrocytic 1 (elliptocytosis 2)| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene… …   Wikipedia

  • Red blood cell — Human red blood cells (6 8μm) Red blood cells (abbreviated RBCs; also referred to as erythrocytes or simply, as red cells[1]) are the most common type of blood cell and the vertebrate organism s principal means of delivering oxygen (O2) to the… …   Wikipedia

  • SPTB — Spectrin, beta, erythrocytic (includes spherocytosis, clinical type I), also known as SPTB, is a human gene.cite web | title = Entrez Gene: SPTB spectrin, beta, erythrocytic (includes spherocytosis, clinical type I)| url = http://www.ncbi.nlm.nih …   Wikipedia

  • HPP — may refer to:*Head Phones President, a Japanese band *Hawaiian Paradise Park, a community on the island of Hawaii *Hereditary pyropoikilocytosis *Hypokalemic periodic paralysis *File extension of C++ header file *Hydroelectric power plant *Holme… …   Wikipedia

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”