propionyl-CoA carboxylase
- propionyl-CoA carboxylase
- pro·pi·o·nyl-CoA car·boxy·lase (proґpe-ə-nəl ko-aґ kahr-bokґsə-lās) [EC 6.4.1.3] an enzyme of the ligase class that catalyzes the carboxylation of propionyl CoA to form methylmalonyl CoA; the reaction is part of the route by which three-carbon compounds from some amino acids and from odd-numbered fatty acids are used as fuels. The enzyme is an oligomer comprising 4α and 4β chains and requires a biotin cofactor. Deficiency of enzyme activity due to a defect in either chain, an autosomal recessive trait, causes propionicacidemia; see also multiple carboxylase deficiency, under carboxylase.
Medical dictionary.
2011.
Look at other dictionaries:
Propionyl-CoA-Carboxylase — Propionyl CoA Carboxylase, α Untereinheit Masse/Länge Primärstruktur 703 Aminosäuren (Mensch) … Deutsch Wikipedia
Propionyl-CoA carboxylase — PCCA redirects here. For other uses, see PCCA (disambiguation). Propionyl CoA carboxylase Identifiers EC number 6.4.1.3 CAS number … Wikipedia
Biotin-(propionyl-CoA-carboxylase (ATP-hydrolysing)) ligase — In enzymology, a biotin [propionyl CoA carboxylase (ATP hydrolysing)] ligase (EC number|6.3.4.10) is an enzyme that catalyzes the chemical reaction:ATP + biotin + apo [propionyl CoA:carbon dioxide ligase (ADP forming)] ightleftharpoons AMP +… … Wikipedia
propionyl-CoA — The coenzyme A thioester derivative of propionic acid; an intermediate in the degradation of l valine, l isoleucine, l threonine, l methionine, and odd chain fatty acid s; a precursor for the synthesis of odd chain fatty acid s; it accumulates in … Medical dictionary
Propionyl-CoA — Chembox new ImageFile = ImageSize = IUPACName = OtherNames = Section1 = Chembox Identifiers CASNo = 317 66 8 PubChem = 1033 SMILES = MeSHName = propionyl coenzyme+A Section2 = Chembox Properties Formula = C24H40N7O17P3S MolarMass = 823.599… … Wikipedia
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Methylcrotonoyl-CoA-Carboxylase — 1 (α Untereinheit) Masse/Länge Primärstruktur 725 AA … Deutsch Wikipedia
Methylcrotonyl-CoA-Carboxylase — Methylcrotonoyl CoA Carboxylase 1 (α Untereinheit) Größe 725 AA Kofaktor Biotin Bezeichner … Deutsch Wikipedia
3-Methylcrotonyl-CoA carboxylase deficiency — Classification and external resources Methylcrotonyl CoA OMIM 210200 … Wikipedia
Propionyl-coenzyme A — Structure de la propionyl CoA Général No CAS … Wikipédia en Français
