isovaleryl-CoA dehydrogenase

isovaleryl-CoA dehydrogenase
iso·val·er·yl-CoA de·hy·dro·gen·ase (i″so-və-lerґəl-ko-aґ de-hiґdro-jən-ās) [EC 1.3.99.10] an enzyme of the oxidoreductase class that catalyzes the dehydrogenation of isovaleryl CoA to 3-methylcrotonyl CoA, using ubiquinone as an electron acceptor. The reaction is a step in the use of leucine as a fuel. Deficiency of the enzyme, an autosomal recessive trait, results in isovalericacidemia.

Medical dictionary. 2011.

Игры ⚽ Поможем решить контрольную работу

Look at other dictionaries:

  • Isovaleryl-CoA dehydrogenase — In enzymology, an isovaleryl CoA dehydrogenase (EC number|1.3.99.10) is an enzyme that catalyzes the chemical reaction:3 methylbutanoyl CoA + acceptor ightleftharpoons 3 methylbut 2 enoyl CoA + reduced acceptorThus, the two substrates of this… …   Wikipedia

  • isovaleryl-CoA — The condensation product of isovaleric acid and coenzyme A; an intermediate in the catabolism of l leucine. SYN: isovalerylcoenzyme A. isovaleryl CoA dehydrogenase an enzyme that participates in the catabolism of l leucine; it converts isovaleryl …   Medical dictionary

  • Isovaleryl-CoA — Chembox new ImageFile=Isovaleryl coenzyme A.svg ImageSize=300px IUPACName= OtherNames= Section1= Chembox Identifiers CASNo=6244 91 3 PubChem=810 SMILES= MeSHName=isovaleryl coenzyme+A Section2= Chembox Properties Formula=C26H44N7O17P3S… …   Wikipedia

  • Isovaleryl coenzyme A dehydrogenase — protein Name=isovaleryl Coenzyme A dehydrogenase caption= width= HGNCid=6186 Symbol=IVD AltSymbols= EntrezGene=3712 OMIM=607036 RefSeq=NM 002225 UniProt=P26440 PDB= ECnumber=1.3.99.10 Chromosome=15 Arm=q Band=14 LocusSupplementaryData=… …   Wikipedia

  • Methylmalonyl-CoA mutase — Rendering based on PDB 2XIJ …   Wikipedia

  • Propionyl-CoA carboxylase — PCCA redirects here. For other uses, see PCCA (disambiguation). Propionyl CoA carboxylase Identifiers EC number 6.4.1.3 CAS number …   Wikipedia

  • Succinate dehydrogenase — (ubiquinone) Subunits: SdhA, SdhB, SdhC and SdhD Identifiers EC number …   Wikipedia

  • Methylcrotonyl-CoA carboxylase — methylcrotonoyl Coenzyme A carboxylase 1 (alpha) Identifiers Symbol MCCC1 Entrez 56922 HUGO …   Wikipedia

  • Methylmalonyl CoA epimerase — Ribbon diagram of methylmalonyl CoA epimerase from Propionibacterium shermanii. From PDB 1JC5 …   Wikipedia

  • Methylglutaconyl-CoA hydratase — AU RNA binding protein/enoyl Coenzyme A hydratase Identifiers Symbol AUH Entrez 549 HUGO …   Wikipedia

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”