isovaleryl-CoA dehydrogenase
- isovaleryl-CoA dehydrogenase
- iso·val·er·yl-CoA de·hy·dro·gen·ase (i″so-və-lerґəl-ko-aґ de-hiґdro-jən-ās) [EC 1.3.99.10] an enzyme of the oxidoreductase class that catalyzes the dehydrogenation of isovaleryl CoA to 3-methylcrotonyl CoA, using ubiquinone as an electron acceptor. The reaction is a step in the use of leucine as a fuel. Deficiency of the enzyme, an autosomal recessive trait, results in isovalericacidemia.
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2011.
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Isovaleryl-CoA dehydrogenase — In enzymology, an isovaleryl CoA dehydrogenase (EC number|1.3.99.10) is an enzyme that catalyzes the chemical reaction:3 methylbutanoyl CoA + acceptor ightleftharpoons 3 methylbut 2 enoyl CoA + reduced acceptorThus, the two substrates of this… … Wikipedia
isovaleryl-CoA — The condensation product of isovaleric acid and coenzyme A; an intermediate in the catabolism of l leucine. SYN: isovalerylcoenzyme A. isovaleryl CoA dehydrogenase an enzyme that participates in the catabolism of l leucine; it converts isovaleryl … Medical dictionary
Isovaleryl-CoA — Chembox new ImageFile=Isovaleryl coenzyme A.svg ImageSize=300px IUPACName= OtherNames= Section1= Chembox Identifiers CASNo=6244 91 3 PubChem=810 SMILES= MeSHName=isovaleryl coenzyme+A Section2= Chembox Properties Formula=C26H44N7O17P3S… … Wikipedia
Isovaleryl coenzyme A dehydrogenase — protein Name=isovaleryl Coenzyme A dehydrogenase caption= width= HGNCid=6186 Symbol=IVD AltSymbols= EntrezGene=3712 OMIM=607036 RefSeq=NM 002225 UniProt=P26440 PDB= ECnumber=1.3.99.10 Chromosome=15 Arm=q Band=14 LocusSupplementaryData=… … Wikipedia
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Succinate dehydrogenase — (ubiquinone) Subunits: SdhA, SdhB, SdhC and SdhD Identifiers EC number … Wikipedia
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Methylglutaconyl-CoA hydratase — AU RNA binding protein/enoyl Coenzyme A hydratase Identifiers Symbol AUH Entrez 549 HUGO … Wikipedia