4-hydroxyphenylpyruvate dioxygenase
- 4-hydroxyphenylpyruvate dioxygenase
- 4-hy·droxy·phen·yl·py·ru·vate di·oxy·gen·ase (hi-drok″se-fen″əl-piґroo-vāt di-okґsə-jən-ās) [EC 1.13.11.27] an enzyme of the oxidoreductase class that catalyzes the oxidation of p-hydroxyphenylpyruvate to homogentisate as a step in the use of tyrosine and phenylalanine as fuels. Deficiency of the enzyme due to heterozygous mutation in the gene encoding it causes hawkinsinuria; that due to homozygous mutation causes tyrosinemia type III.
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4-Hydroxyphenylpyruvate dioxygenase — Protein Name=4 hydroxyphenylpyruvate dioxygenase Symbol=HPD AltSymbols=PPD; HGNCid=5147 Chromosome=12 Arm=q Band=24 qter LocusSupplementaryData= ECnumber=1.13.11.27 OMIM=609695 EntrezGene=3242 RefSeq=NM 002150 UniProt=P327544… … Wikipedia
Cysteine dioxygenase — cysteine dioxygenase, type I Identifiers Symbol CDO1 Entrez 1036 HUGO … Wikipedia
p-hydroxyphenylpyruvate oxidase — p hy·droxy·phen·yl·py·ru·vate ox·i·dase (hi drok″se fen″əl piґroo vāt okґsĭ dās) 4 hydroxyphenylpyruvate dioxygenase … Medical dictionary
List of EC numbers (EC 1) — This list contains a list of EC numbers for the first group, EC 1, oxidoreducatases, placed in numerical order as determined by the Nomenclature Committee of the International Union of Biochemistry and Molecular Biology.EC 1.1 Acting on the CH OH … Wikipedia
Type III tyrosinemia — Infobox Disease Name = PAGENAME Caption = Tyrosine DiseasesDB = 29836 DiseasesDB mult = ICD10 = ICD10|E|70|2|e|70 ICD9 = ICD9|270.2 ICDO = OMIM = 276710 OMIM mult = MedlinePlus = eMedicineSubj = ped eMedicineTopic = 2339 MeshID = D020176 Type III … Wikipedia
Oxygenase — An oxygenase is any enzyme that oxidizes a substrate by transferring the oxygen from molecular oxygen O2 (as in air) to it. The oxygenases form a class of oxidoreductases; their EC number is EC 1.13 or EC 1.14. Oxygenases were discovered in 1955… … Wikipedia
Oxidoreductase — In biochemistry, an oxidoreductase is an enzyme that catalyzes the transfer of electrons from one molecule (the reductant, also called the hydrogen or electron donor) to another (the oxidant, also called the hydrogen or electron acceptor). This… … Wikipedia
Hawkinsinuria — Infobox Disease Name = PAGENAME Caption = Hawkinsin DiseasesDB = 29836 ICD10 = ICD9 = ICDO = OMIM = 276710 OMIM mult = OMIM2|140350 MedlinePlus = eMedicineSubj = eMedicineTopic = MeshID = D020176 Hawkinsinuria, also called 4 Alpha… … Wikipedia
4-hydroxymandelate synthase — In enzymology, a 4 hydroxymandelate synthase (EC number|1.13.11.46) is an enzyme that catalyzes the chemical reaction:4 hydroxyphenylpyruvate + O2 ightleftharpoons 4 hydroxymandelate + CO2Thus, the two substrates of this enzyme are 4… … Wikipedia
Metabolism — Cell metabolism redirects here. For the journal, see Cell Metabolism. Structure of adenosine triphosphate, a central intermediate in energy metabolism Metabolism (from Greek: μεταβολή metabolē , change or Greek: μεταβολισμός metabolismos,… … Wikipedia
