glutaryl-CoA dehydrogenase

glutaryl-CoA dehydrogenase
glu·ta·ryl-CoA de·hy·dro·gen·ase (glooґtə-rəl ko-aґ de-hiґdro-jən-ās) [EC 1.3.99.7] an enzyme of the oxidoreductase class that catalyzes the oxidative decarboxylation of glutaryl CoA, with sequential reduction of FAD and then electron transfer flavoprotein; the reaction is a step in the degradation of lysine, hydroxylysine, and tryptophan. Deficiency of the enzyme, an autosomal recessive trait, causes glutaricaciduria, type I.

Medical dictionary. 2011.

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  • Glutaryl-CoA dehydrogenase — protein Name=glutaryl Coenzyme A dehydrogenase caption= width= HGNCid=4189 Symbol=GCDH AltSymbols= EntrezGene=2639 OMIM=608801 RefSeq=NM 013976 UniProt=Q92947 PDB= ECnumber=1.3.99.7 Chromosome=19 Arm=p Band=13.2 LocusSupplementaryData=Glutaryl… …   Wikipedia

  • glutaryl-CoA — The mono thiol ester of coenzyme A and glutaric acid; an intermediate in l lysine and l tryptophan catabolism. glutaryl CoA dehydrogenase an enzyme that catalyzes the reaction of glutaryl CoA with an acceptor to form crotonoyl …   Medical dictionary

  • Glutaryl-CoA — Chembox new ImageFile=Glutaryl coenzyme A.svg ImageSize=300px IUPACName= OtherNames= Section1= Chembox Identifiers CASNo=3131 84 8 PubChem=3081383 SMILES= MeSHName=Glutaryl coenzyme+A Section2= Chembox Properties Formula=C26H42N7O19P3S… …   Wikipedia

  • Crotonyl-CoA — Strukturformel Allgemeines Name Crotonyl CoA Summenform …   Deutsch Wikipedia

  • Methylmalonyl-CoA mutase — Rendering based on PDB 2XIJ …   Wikipedia

  • Propionyl-CoA carboxylase — PCCA redirects here. For other uses, see PCCA (disambiguation). Propionyl CoA carboxylase Identifiers EC number 6.4.1.3 CAS number …   Wikipedia

  • Succinate dehydrogenase — (ubiquinone) Subunits: SdhA, SdhB, SdhC and SdhD Identifiers EC number …   Wikipedia

  • Methylcrotonyl-CoA carboxylase — methylcrotonoyl Coenzyme A carboxylase 1 (alpha) Identifiers Symbol MCCC1 Entrez 56922 HUGO …   Wikipedia

  • Methylmalonyl CoA epimerase — Ribbon diagram of methylmalonyl CoA epimerase from Propionibacterium shermanii. From PDB 1JC5 …   Wikipedia

  • Methylglutaconyl-CoA hydratase — AU RNA binding protein/enoyl Coenzyme A hydratase Identifiers Symbol AUH Entrez 549 HUGO …   Wikipedia

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