carnitine O-palmitoyltransferase
- carnitine O-palmitoyltransferase
- car·ni·tine O-pal·mi·to·yl·trans·fer·ase (kahrґnĭ-tēn pahl″mĭ-to″əl-transґfər-ās) [EC 2.3.1.21] an enzyme of the transferase class that catalyzes the transfer between coenzyme A and carnitine of long chain fatty acids. Carnitine palmitoyltransferase I transfers the fatty acid to carnitine; the acyl carnitine can then traverse the inner mitochondrial membrane. Once in the matrix, the fatty acid is transferred from carnitine back to coenzyme A by carnitine palmitoyltransferase II; the resultant acyl coenzyme A is a substrate for oxidation. Deficiency of the enzyme is a cause of defective fatty acid oxidation. Written also carnitine palmityltransferase.
Medical dictionary.
2011.
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Carnitine O-palmitoyltransferase — (also called carnitine palmitoyltransferase or carnitine acyltransferase) is a mitochondrial transferase enzyme (EC number|2.3.1.21) involved in the metabolism of palmitoylcarnitine into palmitoyl CoA.MoleculesPathwayHuman forms of CPTThere are… … Wikipedia
Carnitine O-palmitoyltransférase — La carnitine O palmitoyltransférase (CPT) est une enzyme mitochondriale de type transférase (EC 2.3.1.21), impliquée dans le métabolisme de la palmitoylcarnitine en palmitoyl CoA. Une enzyme transférase proche est la carnitine acyltransférase.… … Wikipédia en Français
Carnitine palmitoyltransferase I — carnitine palmitoyltransferase 1A (liver) Identifiers Symbol CPT1A Alt. symbols CPT1 Entrez 1374 … Wikipedia
carnitine acyltransferase — car·ni·tine ac·yl·trans·fer·ase (kahrґnĭ tēn a″səl transґfər ās) carnitine O palmitoyltransferase … Medical dictionary
Carnitine palmitoyltransferase II deficiency — Classification and external resources Carnitine ICD 9 … Wikipedia
Carnitine palmitoyltransferase II — Carnitine palmitoyltransferase II, also known as CPT2, is a human gene.cite web | title = Entrez Gene: CPT2 carnitine palmitoyltransferase II| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene Cmd=ShowDetailView TermToSearch=1376| accessdate … Wikipedia
Carnitine — Systematic (IUPAC) name 3 hydroxy 4 (trimethylazaniumyl)butanoate Clinical data AHFS/Drugs.com … Wikipedia
Carnitine palmitoyltransferase I deficiency — Infobox Disease Name = PAGENAME Caption = Carnitine DiseasesDB = 32535 ICD10 = ICD9 = ICD9|277.85 ICDO = OMIM = 255120 MedlinePlus = eMedicineSubj = ped eMedicineTopic = 321 MeshName = MeshNumber = Carnitine palmitoyltransferase I deficiency is a … Wikipedia
Carnitine-acylcarnitine translocase deficiency — DiseaseDisorder infobox Name = Carnitine acylcarnitine translocase deficiency ICD10 = ICD9 = ICD9|272.8 Carnitine acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long… … Wikipedia
Carnitine O-octanoyltransferase — In enzymology, a carnitine O octanoyltransferase (EC number|2.3.1.137) is an enzyme that catalyzes the chemical reaction:octanoyl CoA + L carnitine ightleftharpoons CoA + L octanoylcarnitineThus, the two substrates of this enzyme are octanoyl CoA … Wikipedia
