- lipogranulomatosis
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- disseminated l. a form of mucolipodosis, developing soon after birth because of deficiency of ceramidase; characterized by swollen joints, subcutaneous nodules, lymphadenopathy, and accumulation in lysosomes of affected cells of PAS-positive lipid consisting of ceramide. SYN: Farber disease, Farber syndrome.
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n.an abnormality of lipid metabolism causing deposition of yellowish nodules in the skin.* * *
lipo·gran·u·lo·ma·to·sis (lip″o-gran″u-lo-mə-toґsis) a condition of faulty lipid metabolism in which yellow nodules of lipoid matter are deposited in the skin and mucosae, giving rise to granulomatous reactions.
Medical dictionary. 2011.