- incontinentia
- SYN: incontinence. [L.]- i. pigmenti [MIM*146150, MIM*308300, and MIM*308310] a rare genodermatosis characterized by hyperpigmented lesions in linear, zebra stripe, and other bizarre configurations following the lines of Blaschko; occasionally accompanied by other developmental anomalies of the eyes, teeth, nails, skeleton, nails, heart. The dermatologic features involve four stages: stage I is characterized by erythema, vesicles, and pustules; stage II by papules, verrucous lesions, and hyperkeratosis; stage III by hyperpigmentation; and stage IV by pallor, atrophy, and scarring. Historically, there were thought to be two forms: 1) the sporadic type of i. pigmenti (IP1), which is now known to be hypomelanosis of Ito and 2) the familial type (IP2), which is X-linked dominant and a genetic lethal in males. SEE ALSO: hypomelanosis of Ito. SYN: Bloch-Sulzberger disease, Bloch-Sulzberger syndrome.- i. pigmenti achromians [MIM*146150] SYN: hypomelanosis of Ito.
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in·con·ti·nen·tia (in-kon″tĭ-nenґshə) [L.] incontinence.
Medical dictionary. 2011.