3-methylcrotonylglycine

3-methylcrotonylglycine
3-meth·yl·cro·ton·yl·gly·cine (meth″əl-kro″to-nəl-gliґsēn) a conjugate of 3-methylcrotonic acid and glycine, formed and excreted in excess in the urine when 3-methylcrotonoyl-CoA carboxylase activity is impaired.

Medical dictionary. 2011.

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  • 3-methylcrotonyl CoA carboxylase deficiency — 3 meth·yl·cro·to·nyl CoA car·box·y·lase de·fi·cien·cy (meth″əl kroґtə nil″ ko aґ kahr bokґsə lās) an autosomal recessive aminoacidopathy due to deficiency of methylcrotonoyl CoA carboxylase, which can result from… …   Medical dictionary

  • β-methylcrotonylglycinuria — β meth·yl·cro·to·nyl·gly·cin·u·ria (meth″əl kro″to nəl gli″sĭ nuґre ə) 3 methylcrotonyl CoA carboxylase deficiency. 2. excretion of 3 methylcrotonylglycine in the urine, as occurs in 3 methylcrotonyl CoA …   Medical dictionary

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